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2025
08-17

胰腺囊性病变影像分类诊断​

作者:stari

来源:1影1世界

胰腺囊性病变影像分类诊断

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在胰腺所有肿瘤中,囊性肿瘤约占20%,胰腺囊性病变较多,良性、恶性都有,有些影像学特征互有重叠,给鉴别诊断带来困难。

胰腺内囊性病变种类

临床上最常见的胰腺囊性肿瘤主要包括浆液性囊腺瘤、黏液性囊性肿瘤和导管内乳头状黏液性肿瘤等,占整个胰腺囊性肿瘤的90%左右。

其它少见的,还有胰腺原发实质性肿瘤囊性变,胰腺转移性肿瘤囊性变,以及一些囊性的肿瘤样病变。

具体分类,思维导图总结如下:

胰腺囊性肿瘤影像学特点

胰腺囊性肿瘤,大部分位于腹腔后壁的腹膜外,由于其生长位置很深,几乎没有临床症状,很难早期发现,大多是检查时偶然发现的。

临床症状的缺如,加上化验指标的非特异性,给这类肿瘤早期诊断带来很大困难。

其中,浆液性囊腺瘤是良性的;实性假乳头状瘤则是低到中度恶性肿瘤;而导管内黏液性乳头状瘤、黏液性囊腺瘤则表现为中到高度恶性的特征。

不同肿瘤有不同的好发年龄,和好发性别,所以在临床上有一些特殊的称呼。

比如,浆液性囊腺瘤,好发于老年女性,大家习惯叫它“奶奶瘤”(SCN);而黏液性囊腺瘤好发于中年女性,大家习惯叫它“妈妈瘤”(MCN);实性假乳头状瘤,则是青年女性多发,所以也叫“女儿瘤”(SPN)。

看似复杂、繁多,其实主要是这四种,大约占到90%多。

鉴别诊断:

然而,胰腺囊性肿瘤间鉴别,以及与胰腺囊性病变、胰腺肿瘤的囊性变的鉴别,存在难点,CT表现或征象有一定的重叠。Sahani 等依据CT特征,分为四型。

I型,

包括假性囊肿(最常见)、真性囊肿、大囊型浆液性囊腺瘤、极少部分黏液性囊腺瘤、分支型导管内乳头状黏液性肿瘤、Hippel-Lindau氏综合征等等,胰腺呈单发或多发囊样病变。

结合曾有胰腺炎病史,则提示为假性囊肿。

如多平面重建或MRCP显示胰腺主胰管与囊性病变相通,则为分支型导管内乳头状粘液性肿瘤机会显著提高。

II型,

只见于良性小囊型浆液性囊腺瘤,有典型CT征象。

III型,

大囊型浆液性囊腺瘤和黏液性囊腺瘤(癌)均可相似表现,难以鉴别。

IV型,

包括黏液性囊腺癌、实质性假乳头状肿瘤、非功能性胰腺神经内分泌肿瘤、腺泡细胞囊腺癌和主胰管型/混合型导管内乳头状黏液性肿瘤。

这一类,CT鉴别有难度,确诊依赖病理。

那么 ,这种情况下,偶然发现胰腺囊性病变,该怎么处理呢?下面我们总结了临床诊治流程图,希望对大家有所帮助。

由此可以看出,胰腺内囊性病变,和发病年龄、发病部位有密切关系,并且,各自形态学上、病理特点上、生物学行为上各不相同,临床预后也各不相同,所以鉴别诊断应充分考虑这些因素。上面这幅图,形象地展示了胰腺内各类囊性病变的形态学特点,和好发部位,有助于理解其影像诊断与鉴别诊断。

-待续-

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